Diseases with tau-based neurofibrillary pathology
Alzheimer's disease
Amyotrophic lateral sclerosis/parkinsonism–dementia complexa
Argyrophilic grain dementiaa
Corticobasal degenerationa
Creutzfeldt-Jakob disease
Dementia pugilisticaa
Diffuse neurofibrillary tangles with calcificationa
Down's syndrome
Frontotemporal dementia with parkinsonism linked to chromosome 17a
Gerstmann-Sträussler-Scheinker disease
Hallervorden-Spatz disease
Myotonic dystrophy
Niemann-Pick disease, type C
Non-Guamanian motor neuron disease with neurofibrillary tangles
Pick's diseasea
Postencephalitic parkinsonism
Prion protein cerebral amyloid angiopathy
Progressive subcortical gliosisa
Progressive supranuclear palsya
Subacute sclerosing panencephalitis
Tangle only dementia
Lee VM, Goedert M, Trojanowski JQ. Neurodegenerative tauopathies. Annu Rev Neurosci. 2001;24:1121-5
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